Ependymoma of the spinal cord with multiple intradural extramedullary ependymomas: The first case report and literature review


      • we report the first case of exophytic ependymoma of the spinal cord with multiple IDEM ependymomas.
      • we proposed the most likely pathogenesis of this case.
      • we reviewed exophytic intramedullary ependymoma, multiple non-conus, and non-filum intradural extramedullary (IDEM) ependymomas and analyzed the their clinical features, imaging features, treatment and prognosis.


      Ependymomas are the most prevalent intramedullary neoplasms in adults. Few cases have been reported on exophytic intramedullary ependymoma or multiple non-conus, and non-filum intradural extramedullary (IDEM) ependymomas. Here, we reported a 30-years old female with exophytic ependymoma in T10-11 and multiple IDEM ependymomas in T3–S2 and who's condition ultimately improved. This is the first case of exophytic ependymoma of the spinal cord with multiple IDEM ependymomas.


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