Highlights
- •Hypertrophic osteoarthropathy can be primary or secondary.
- •Pachydermoperiostosis is the primary form of HOA.
- •Pachydermoperiostosis can be associated with systemic manifestations.
- •WB-DWIBS can be used in systemic processes to detect extent of disease involvement.
- •WB-DWIBS may be useful in pachydermoperiostosis to detect systemic manifestations.
Abstract
Hypertrophic osteoarthropathy (HOA) is a disease characterized by abnormal skin findings
and bone deformities related to subperiosteal bone formation. The disease can be associated
with major systemic manifestations (secondary form) or present with absent or less
prominent systemic signs and symptoms (primary form). The primary form is called pachydermoperiostosis
(PDP). Whole body diffusion weighted imaging with background suppression (WB-DWIBS)
is a magnetic resonance imaging (MRI) technique that has been used to highlight whole
body involvement in various entities by suppressing background body signals, and is
commonly used in oncologic work-ups. In this paper, we present the case of a 23-year-old
male presenting with normocytic anemia and coarse facial features, as well as biological
anomalies, and we report the use of WB-DWIBS in establishing the patient's diagnosis
of PDP.
Keywords
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Article info
Publication history
Published online: January 03, 2022
Accepted:
December 9,
2021
Received in revised form:
November 20,
2021
Received:
August 25,
2021
Identification
Copyright
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