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Ossified dysraphic hamartoma with lipomyelocoele/lipomyelomeningocoele—A rare radiological entity

      Highlights

      • Spinal lipomas associated with closed spinal dysraphism are better described as spinal hamartomas.
      • Spinal hamartomas contain unencapsulated and infiltrating fat along with other heterotopic soft tissue.
      • Presence of bone in this setting is called ossified dysraphic hamartoma.
      • Knowledge of presence of well-formed bone helps in surgical planning.

      Abstract

      Traditionally the presence of fat in closed spinal dysraphism has been referred to as spinal lipoma. Recent reports suggest that these spinal lesions are better described as spinal hamartomas due to the unencapsulated and infiltrating nature of the fat and presence of other heterotopic soft tissue. The presence of ossified bone in spinal hamartomas referred to as ossified dysraphic hamartoma, is extremely rare with only three case reports in literature, all associated with lipomyeloceles, none with lipomyelomeningoceles. We present three cases of ossified dysraphic hamartoma, two of them associated with lipomyelomeningoceles, reviewing imaging features on CT and MRI.

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