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Desmoplastic small round cell tumor of the kidney with unusual imaging features

  • Author Footnotes
    1 Present address: Department of Radiology and Radiological Sciences, Medical University of South Carolina, MSC 323, 96 Jonathan Lucas St., Charleston, SC 29425.
    Meryle J. Eklund
    Correspondence
    Corresponding author. Tel.: +1-843-792-4033; fax: +1-843-792-5067.
    Footnotes
    1 Present address: Department of Radiology and Radiological Sciences, Medical University of South Carolina, MSC 323, 96 Jonathan Lucas St., Charleston, SC 29425.
    Affiliations
    Department of Radiology and Imaging Sciences, Emory University and Children’s Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA
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  • Caitlin Cundiff
    Affiliations
    Department of Pathology, Emory University and Children’s Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA
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  • Bahig M. Shehata
    Affiliations
    Department of Pathology and Pediatrics, Emory University and Children’s Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA
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  • Adina L. Alazraki
    Affiliations
    Department of Radiology and Imaging Sciences, Emory University and Children’s Healthcare of Atlanta, Egleston, 1405 Clifton Rd NE, Atlanta, GA 30322, USA
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  • Author Footnotes
    1 Present address: Department of Radiology and Radiological Sciences, Medical University of South Carolina, MSC 323, 96 Jonathan Lucas St., Charleston, SC 29425.

      Abstract

      Desmoplastic small round cell tumor (DSRCT) is a rare, high-grade sarcoma seen in children and young adults. DSRCT of the kidney is extremely uncommon, but has been described in both pediatric and adult populations. Here we present an unusual manifestation of renal DSRCT in a boy whose imaging studies revealed a well-circumscribed mass confined to the urinary collecting system, rather than a large aggressive-appearing mass typically associated with DSRCT, which highlights the varied clinical and imaging features of this disease.

      Keywords

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