Abstract
Desmoplastic small round cell tumor (DSRCT) is a rare, high-grade sarcoma seen in
children and young adults. DSRCT of the kidney is extremely uncommon, but has been
described in both pediatric and adult populations. Here we present an unusual manifestation
of renal DSRCT in a boy whose imaging studies revealed a well-circumscribed mass confined
to the urinary collecting system, rather than a large aggressive-appearing mass typically
associated with DSRCT, which highlights the varied clinical and imaging features of
this disease.
Keywords
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References
- Non-Wilms' renal tumors in children.Urol Clin N Am. 2000; 27 (ix): 463-469
- Intra-abdominal desmoplastic small round-cell tumour: multiphase CT findings in two children.Pediatr Radiol. 2003; 33: 418-421
- Desmoplastic small round cell tumor of the kidney in a pediatric patient: sonographic and multiphase CT findings.AJR Am J Roentgenol. 2005; 185: 1347-1349
- Diagnostic pitfalls of differentiating desmoplastic small round cell tumor (DSRCT) from Wilms tumor (WT): overlapping morphologic and immunohistochemical features.Am J Surg Pathol. 2014; 38: 1220-1226
- Desmoplastic small round cell tumor of the kidney in childhood.Am J Surg Pathol. 2007; 31 ([PubMed PMID:17414105]): 576-584
- Desmoplastic small round cell tumor of the kidney.Am J Surg Pathol. 2004; 28: 1379-1383
- Desmoplastic small round cell tumor of the kidney mimicking Wilms tumor: a case report and review of the literature.Appl Immunohistochem Mol Morphol. 2009; 17: 557-562
- Primary desmoplastic small round cell tumor of the kidney: a case report in a 14-year-old girl with molecular confirmation.Pediatr Dev Pathol. 2007; 10: 320-324
Article info
Publication history
Published online: May 07, 2015
Accepted:
May 2,
2015
Received:
March 27,
2015
Identification
Copyright
© 2015 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
