Case Report| Volume 39, ISSUE 4, P677-681, July 2015

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Cervical dural arteriovenous malformation and large epidural venous varices in a rare adult presentation of congenital vascular bone syndrome


      61-year-old male presented with shortness of breath and chest pain. Workup for acute myocardial infarction was negative; however, computed tomography angiography visualized what a vascular malformation within the cervical spinal canal. Given the patient's history of Servelle–Martorell syndrome, neurovascular imaging was performed. We present the unique vascular findings of a right thyrocervical trunk-based dural arteriovenous malformation (dAVM) and a large epidural venous varix. The cervical dAVM induced intervertebral foraminal widening and polyradiculopathy, representing a rare adult case of congenital vascular bone syndrome.


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