Abstract
Light chain deposition disease (LCDD) is a rare clinicopathologic entity first described
in 1976 and is characterized by a monoclonal gammopathy resulting in nonamyloid immunoglobulin
light chain tissue deposition. Only four cases of intracerebral LCDD have been previously
reported, all in the setting of a known plasma cell dyscrasia or in the presence of
local mature plasma cells. We present the first case of intracranial LCDD in the absence
of a known plasma cell dyscrasia or local mature plasma cells.
Keywords
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Article info
Publication history
Published online: July 02, 2014
Accepted:
June 26,
2014
Received in revised form:
June 24,
2014
Received:
April 11,
2014
Footnotes
☆Funding: J.P.Y was generously supported in part by a NIBIB T32 Institutional Training Grant (T32 EB001631).
Identification
Copyright
© 2014 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
