Abstract
Lymphangioleiomyomatosis (LAM) is a rare disorder that predominantly affects the lung
parenchyma of young women and it's characterized by pulmonary cyst. Tuberous sclerosis
complex (TSC) is a rare genetic disorder presenting with hamartomas and neurologic
symptoms. The two renal pathologies most commonly seen in TSC are angiomyolipomas
and cysts; less commonly, TSC co-exist with polycystic kidney disease. In this report
is described an uncommon case of a patient with broncheoalveolar carcinoma, pulmonary
LAM and TSC with polycystic kidney disease.
Keywords
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Article info
Publication history
Published online: May 19, 2010
Accepted:
April 2,
2010
Received:
February 20,
2010
Identification
Copyright
© 2011 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
