Abstract
Susac syndrome is a rare neurologic disorder first described by Susac et al. in 1979.
Clinically, Susac syndrome consists of a triad including encephalopathy, branch retinal
artery occlusion, and sensorineural hearing loss. Microinfarction is believed to be
the basic histologic feature and MR is considered the best imaging modality. This
case documents the typical imaging findings of Susac syndrome, as well as the unique
MR imaging finding of cranial nerve enhancement.
Keywords
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References
- Micoangiopathy of the brain and retina.Neurology. 1979; 29: 313-316
- Microangiopathy of the brain and retina (Susac's syndrome): two patients with atypical features.Neurology. 1995; 45: 1225-1226
- Susac's syndrome.AJNR Am J Neuroradiol. 2004; 25: 351-352
- Susac's syndrome: 1975–2005 microangiopathy/autoimmune endotheliopathy.J Neurol Sci. 2007; 257 ([Epub 2007 Feb 28]): 270-272
- Susac syndrome: report of four cases and review of literature.AJNR Am J Neuroradiol. 2004; 25: 382-388
- Microangiopathy of the brain, retina and inner ear (Susac's Syndrome) in an adolescent female presenting as acute disseminated encephalomyelitis.Pediatrics. 2004; 114: 226-281
- MRI of Susac's syndrome.AJR Am J Roentgenol. 2005; 184: 1688-1690
- MRI findings in Susac's syndrome.Neurology. 2003; 61: 1783-1787
- Evolution of lesions in Susac syndrome at serial MR imaging with diffusion-weighted imaging and apparent diffusion coefficient values.AJNR Am J Neuroradiol. 2004; 25: 706-713
- Diffusion tensor imaging demonstrates fiber impairment in Susac syndrome.Neurology. 2008; 70: 1867-1869
- Treatment of Susac's syndrome.Curr Treat Options Neurol. 2008; 10: 67-74
- The spectrum of Susac's syndrome.Neurol Sci. 2009; 30 ([Epub 2009 Jan 15]): 59-64
Article info
Publication history
Published online: October 26, 2009
Accepted:
May 6,
2009
Received:
April 25,
2009
Identification
Copyright
© 2010 Elsevier Inc. Published by Elsevier Inc. All rights reserved.