Abstract
Persistent müllerian duct syndrome (PMDS) is a rare form of male pseudohermaphroditism.
Two anatomic forms are described in this syndrome, the male and the female one; the
second one is usually associated with bilateral cryptorchidism.
About 150 cases are reported in literature; most of them are focused on anatomical,
genetic, and surgical aspects. Radiological imaging features, important for diagnosis
and therapy planification, are rarely reported.
We describe a case of a female type of PMDS studied with multidetector computed tomography.
Keywords
To read this article in full you will need to make a payment
Purchase one-time access:
Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online accessOne-time access price info
- For academic or personal research use, select 'Academic and Personal'
- For corporate R&D use, select 'Corporate R&D Professionals'
Subscribe:
Subscribe to Clinical ImagingAlready a print subscriber? Claim online access
Already an online subscriber? Sign in
Register: Create an account
Institutional Access: Sign in to ScienceDirect
References
- Hernia uteris inguinalis beim manne.Acta Chir Scand. 1939; 83: 231-239
- Persistent Müllerian duct syndrome with seminoma: CT findings.AJR Am J Roentgenol. 2000; 174: 102-104
- US and MRI in a case of persistent Müllerian duct syndrome.Pediatr Radiol. 1998; 28: 865-867
- Germinal cell tumors of the testis in cryptorchids.J Exp Clin Cancer Res. 1998; 17: 409-412
- Persistent Müllerian duct syndrome with or without transverse testicular ectopia and testis tumors.Br J Urol. 1997; 79: 122-126
- Transverse testicular ectopia in a man with persistent Müllerian duct syndrome.Arch Pathol Lab Med. 1994; 118: 752-755
- Persistent Müllerian duct syndrome with transverse testicular ectopia and spermatogenesis.J Urol. 1992; 147: 1615-1617
- Radiological findings in three cases of persistent müllerian duct syndrome.Pediatr Radiol. 1993; 23: 55-56
- The persistent müllerian duct syndrome: a molecular approach.J Clin Endocrinol Metab. 1989; 68: 48-52
- Surgical and genetic aspects of persistent müllerian duct syndrome.J Ped Surg. 1994; 29: 61-65
- Persistent Müllerian duct syndrome suggested by magnetic resonance imaging.Radiat Med. 2003; 21: 277-279
- Persistent Müllerian duct syndrome.Radiographics. 2003; 23: 309-313
- Embryology and endocrinology of genital development.Baillieres Clin Endocrinol Metab. 1998; 12: 17-33
- Clinical aspects and molecular genetics of the persistent müllerian duct syndrome.Clin Endocrinol. 1997; 47: 137-144
- Persistence of müllerian derivatives in males.Am J Med Genet. 1999; 89: 218-223
- Surgical management of persistent müllerian duct syndrome.Urology. 1997; 49: 941-945
- Persistent müllerian duct syndrome: review and report of 3 cases.Br J Urol. 1985; 57: 548-551
- Persistent müllerian duct syndrome: reports of two cases.Scand J Urol Nephrol. 1993; 27: 563-565
- A case of clear cell adenocarcinoma of the Müllerian duct in persistent Müllerian duct syndrome.Am J Surg Pathol. 2002; 26: 1231-1234
Article info
Publication history
Published online: February 27, 2008
Accepted:
November 13,
2007
Received:
October 25,
2007
Identification
Copyright
© 2008 Elsevier Inc. Published by Elsevier Inc. All rights reserved.
