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Female form of persistent müllerian duct syndrome: MDCT findings

Published:February 27, 2008DOI:https://doi.org/10.1016/j.clinimag.2007.11.002

      Abstract

      Persistent müllerian duct syndrome (PMDS) is a rare form of male pseudohermaphroditism.
      Two anatomic forms are described in this syndrome, the male and the female one; the second one is usually associated with bilateral cryptorchidism.
      About 150 cases are reported in literature; most of them are focused on anatomical, genetic, and surgical aspects. Radiological imaging features, important for diagnosis and therapy planification, are rarely reported.
      We describe a case of a female type of PMDS studied with multidetector computed tomography.

      Keywords

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