Abstract
Melorheostosis is a rare bone disease of unknown etiology. It is characterized by
tense and erythematous skin, contractures and shortening of the affected limbs. Radiographs
reveal hyperostosis in long bones resembling melting wax, and spotty or patchy endostic
deposits in short bones. An 11-year-old girl showed, since birth, contractural deformities
in the right hand without bone abnormalities. At the age of 12 months, she complained
of soft tissue tightness in the right buttock. At 3 years, limitation of flexion and
extension of the right knee was evident. Radiographs revealed findings typical of
melorheostosis.
Keywords
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Article info
Publication history
Received:
June 18,
2001
Identification
Copyright
© 2002 Elsevier Science Inc. Published by Elsevier Inc. All rights reserved.
