Abstract
Lymphangioleiomyomatosis (LAM) is a rare idiopathic disease characterized by hamartomatous
smooth muscle proliferation of the lymph node, lymphatics, blood vessels as well as
airways within the lungs, mediastinum and abdomen. It exclusively affects women during
the reproductive period. Though extrapulmonary manifestations have been reported,
the initial presentation of LAM as abdominal pain is extremely rare. To our knowledge,
there are only three cases with LAM presenting first with abdominal symptoms so far
[Chest 106 (1994) 267; Eur J Radiol 14 (1992) 192; Eur J Surg 157 (1991) 36]. We describe
a case of LAM suffering from abdominal pain followed by pulmonary symptoms and the
diagnosis was not made until pathohistological examination.
Keywords
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Article info
Publication history
Received:
June 18,
2001
Identification
Copyright
© 2003 Elsevier Science Inc. Published by Elsevier Inc. All rights reserved.
